Uniprot ID | Q9UJ83 |
Uniprot Name | HACL1_HUMAN |
Taxonomy ID | 9606 |
Sequence |
M
P
D
S
N
F
A
E
R
S
E
E
Q
V
S
G
A
K
V
I
A
Q
A
L
K
T
Q
D
V
E
Y
I
F
G
I
V
G
I
P
V
T
E
I
A
I
A
A
Q
Q
L
G
I
K
Y
I
G
M
R
N
E
Q
A
A
C
Y
A
A
S
A
I
G
Y
L
T
S
R
P
G
V
C
L
V
V
S
G
P
G
L
I
H
A
L
G
G
M
A
N
A
N
M
N
C
W
P
L
L
V
I
G
G
S
S
E
R
N
Q
E
T
M
G
A
F
Q
E
F
P
Q
V
E
A
C
R
L
Y
T
K
F
S
A
R
P
S
S
I
E
A
I
P
F
V
I
E
K
A
V
R
S
S
I
Y
G
R
P
G
A
C
Y
V
D
I
P
A
D
F
V
N
L
Q
V
N
V
N
S
I
K
Y
M
E
R
C
M
S
P
P
I
S
M
A
E
T
S
A
V
C
T
A
A
S
V
I
R
N
A
K
Q
P
L
L
I
I
G
K
G
A
A
Y
A
H
A
E
E
S
I
K
K
L
V
E
Q
Y
K
L
P
F
L
P
T
P
M
G
K
G
V
V
P
D
N
H
P
Y
C
V
G
A
A
R
S
R
A
L
Q
F
A
D
V
I
V
L
F
G
A
R
L
N
W
I
L
H
F
G
L
P
P
R
Y
Q
P
D
V
K
F
I
Q
V
D
I
C
A
E
E
L
G
N
N
V
K
P
A
V
T
L
L
G
N
I
H
A
V
T
K
Q
L
L
E
E
L
D
K
T
P
W
Q
Y
P
P
E
S
K
W
W
K
T
L
R
E
K
M
K
S
N
E
A
A
S
K
E
L
A
S
K
K
S
L
P
M
N
Y
Y
T
V
F
Y
H
V
Q
E
Q
L
P
R
D
C
F
V
V
S
E
G
A
N
T
M
D
I
G
R
T
V
L
Q
N
Y
L
P
R
H
R
L
D
A
G
T
F
G
T
M
G
V
G
L
G
F
A
I
A
A
A
V
V
A
K
D
R
S
P
G
Q
W
I
I
C
V
E
G
D
S
A
F
G
F
S
G
M
E
V
E
T
I
C
R
Y
N
L
P
I
I
L
L
V
V
N
N
N
G
I
Y
Q
G
F
D
T
D
T
W
K
E
M
L
K
F
Q
D
A
T
A
V
V
P
P
M
C
L
L
P
N
S
H
Y
E
Q
V
M
T
A
F
G
G
K
G
Y
F
V
Q
T
P
E
E
L
Q
K
S
L
R
Q
S
L
A
D
T
T
K
P
S
L
I
N
I
M
I
E
P
Q
A
T
R
K
A
Q
D
F
H
W
L
T
R
S
N
M
|
Cofactor |
COFACTOR: Name=Mg(2+); Xref=ChEBI:CHEBI:18420; Note=Binds 1 Mg(2+) ion per subunit.; COFACTOR: Name=thiamine diphosphate; Xref=ChEBI:CHEBI:58937; Note=Binds 1 thiamine pyrophosphate per subunit.; |
Active site |
No current data |
Pfam |
PF02775
PF00205
PF02776
|
InterPro |
IPR029035
IPR029061
IPR012000
IPR012001
IPR011766
|