TitleDatePubMed ID
A Spontaneous Missense Mutation in Branched Chain Keto Acid Dehydrogenase Kinase in the Rat Affects Both the Central and Peripheral Nervous Systems.201627472223
Octanoic acid promotes branched-chain amino acid catabolisms via the inhibition of hepatic branched-chain alpha-keto acid dehydrogenase kinase in rats.2015 Sep26104959
Benzothiophene carboxylate derivatives as novel allosteric inhibitors of branched-chain α-ketoacid dehydrogenase kinase.2014 Jul 2524895126
Two novel mutations in the BCKDK (branched-chain keto-acid dehydrogenase kinase) gene are responsible for a neurobehavioral deficit in two pediatric unrelated patients.2014 Apr24449431
PGC-1α-mediated branched-chain amino acid metabolism in the skeletal muscle.201424638054
Structure-based design and mechanisms of allosteric inhibitors for mitochondrial branched-chain α-ketoacid dehydrogenase kinase.2013 Jun 1123716694
Stimulation of rat liver branched-chain alpha-keto acid dehydrogenase activity by low doses of bezafibrate.2013 Apr 523485652
Mutations in BCKD-kinase lead to a potentially treatable form of autism with epilepsy.2012 Oct 1922956686
Regulation of hepatic branched-chain alpha-keto acid dehydrogenase kinase in a rat model for type 2 diabetes mellitus at different stages of the disease.2010 Mar 520138840
Inhibition of branched-chain alpha-ketoacid dehydrogenase kinase by thiamine pyrophosphate at different potassium ionic levels.2009 May19420697