NADH dehydrogenase [ubiquinone] iron-sulfur protein 8, mitochondrial
Name | NADH dehydrogenase [ubiquinone] iron-sulfur protein 8, mitochondrial |
---|---|
Synonyms | 1.6.5.3 CI-23kD Complex I-23kD NADH-ubiquinone oxidoreductase 23 kDa subunit TYKY subunit |
Gene Name | NDUFS8 |
Organism | Human |
Amino acid sequence | >lcl|BSEQ0009891|NADH dehydrogenase [ubiquinone] iron-sulfur protein 8, mitochondrial MRCLTTPMLLRALAQAARAGPPGGRSLHSSAVAATYKYVNMQDPEMDMKSVTDRAARTLL WTELFRGLGMTLSYLFREPATINYPFEKGPLSPRFRGEHALRRYPSGEERCIACKLCEAI CPAQAITIEAEPRADGSRRTTRYDIDMTKCIYCGFCQEACPVDAIVEGPNFEFSTETHEE LLYNKEKLLNNGDKWEAEIAANIQADYLYR |
Number of residues | 210 |
Molecular Weight | 23704.795 |
Theoretical pI | 6.27 |
GO Classification |
Functions
4 iron, 4 sulfur cluster binding NADH dehydrogenase (ubiquinone) activity metal ion binding Processes
mitochondrial respiratory chain complex I assembly respiratory electron transport chain mitochondrial electron transport, NADH to ubiquinone response to oxidative stress small molecule metabolic process cellular metabolic process Components
mitochondrial respiratory chain complex I mitochondrion mitochondrial matrix |
General Function | Nadh dehydrogenase (ubiquinone) activity |
Specific Function | Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone (By similarity). May donate electrons to ubiquinone. |
Transmembrane Regions | |
GenBank Protein ID | 1935056 |
UniProtKB ID | O00217 |
UniProtKB Entry Name | NDUS8_HUMAN |
Cellular Location | Mitochondrion |
Gene sequence | >lcl|BSEQ0009892|NADH dehydrogenase [ubiquinone] iron-sulfur protein 8, mitochondrial (NDUFS8) ATGCGCTGCCTGACCACGCCTATGCTGCTGCGGGCCCTGGCCCAGGCTGCACGTGCAGGA CCTCCTGGTGGCCGGAGCCTCCACAGCAGTGCAGTGGCAGCCACCTACAAGTATGTGAAC ATGCAGGATCCCGAGATGGACATGAAGTCAGTGACTGACCGGGCAGCCCGCACCCTGCTG TGGACTGAGCTCTTCCGAGGCCTGGGCATGACCCTGAGCTACCTGTTCCGGGAACCGGCC ACCATCAACTACCCGTTCGAGAAGGGCCCGCTGAGCCCTCGCTTCCGTGGGGAGCATGCG CTGCGCCGGTACCCATCCGGGGAGGAGCGTTGCATTGCCTGCAAGCTCTGCGAGGCCATC TGCCCCGCCCAGGCCATCACCATCGAGGCTGAGCCAAGAGCTGATGGCAGCCGCCGGACC ACCCGCTATGACATCGACATGACCAAGTGCATCTACTGCGGCTTCTGCCAGGAGGCCTGT CCCGTGGATGCCATCGTCGAGGGCCCCAACTTTGAGTTCTCCACGGAGACCCATGAGGAG CTGCTGTACAACAAGGAGAAGTTGCTCAACAACGGGGACAAGTGGGAGGCCGAGATCGCC GCCAACATCCAGGCTGACTACTTGTATCGGTGA |
GenBank Gene ID | U65579 |
GeneCard ID | None |
GenAtlas ID | NDUFS8 |
HGNC ID | HGNC:7715 |
Chromosome Location | 11 |
Locus | 11q13 |
References |
|
Related FRC
FRCD ID | Name | Exact Mass | Structure |
---|---|---|---|
Thallium |
239.83 |