Pyruvate dehydrogenase E1 component subunit alpha, testis-specific form, mitochondrial
| Name | Pyruvate dehydrogenase E1 component subunit alpha, testis-specific form, mitochondrial |
|---|---|
| Synonyms | 1.2.4.1 PDHAL PDHE1-A type II |
| Gene Name | PDHA2 |
| Organism | Human |
| Amino acid sequence | >lcl|BSEQ0001215|Pyruvate dehydrogenase E1 component subunit alpha, testis-specific form, mitochondrial MLAAFISRVLRRVAQKSARRVLVASRNSSNDATFEIKKCDLYLLEEGPPVTTVLTRAEGL KYYRMMLTVRRMELKADQLYKQKFIRGFCHLCDGQEACCVGLEAGINPSDHVITSYRAHG VCYTRGLSVRSILAELTGRRGGCAKGKGGSMHMYTKNFYGGNGIVGAQGPLGAGIALACK YKGNDEICLTLYGDGAANQGQIAEAFNMAALWKLPCVFICENNLYGMGTSTERAAASPDY YKRGNFIPGLKVDGMDVLCVREATKFAANYCRSGKGPILMELQTYRYHGHSMSDPGVSYR TREEIQEVRSKRDPIIILQDRMVNSKLATVEELKEIGAEVRKEIDDAAQFATTDPEPHLE ELGHHIYSSDSSFEVRGANPWIKFKSVS |
| Number of residues | 388 |
| Molecular Weight | 42932.855 |
| Theoretical pI | 8.56 |
| GO Classification |
Functions
pyruvate dehydrogenase (acetyl-transferring) activity Processes
tricarboxylic acid cycle glucose metabolic process acetyl-CoA biosynthetic process from pyruvate pyruvate metabolic process Components
pyruvate dehydrogenase complex nucleus mitochondrial matrix |
| General Function | Pyruvate dehydrogenase (acetyl-transferring) activity |
| Specific Function | The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2), and thereby links the glycolytic pathway to the tricarboxylic cycle. |
| Transmembrane Regions | |
| GenBank Protein ID | 190790 |
| UniProtKB ID | P29803 |
| UniProtKB Entry Name | ODPAT_HUMAN |
| Cellular Location | Mitochondrion matrix |
| Gene sequence | >lcl|BSEQ0010423|Pyruvate dehydrogenase E1 component subunit alpha, testis-specific form, mitochondrial (PDHA2) ATGCTGGCCGCCTTCATCTCCCGCGTGTTGAGGCGAGTTGCCCAGAAATCAGCTCGCAGA GTGCTGGTGGCATCCCGTAACTCCTCAAATGACGCTACATTTGAAATTAAGAAATGTGAT CTTTATCTGTTGGAAGAGGGTCCCCCTGTCACTACAGTGCTCACTAGGGCGGAGGGGCTT AAATACTACAGGATGATGCTGACTGTTCGCCGCATGGAATTGAAGGCAGATCAGCTGTAC AAACAGAAATTCATTCGCGGTTTCTGTCACCTGTGCGATGGTCAGGAAGCTTGTTGCGTG GGCCTTGAGGCCGGCATAAACCCCTCGGATCACGTCATTACATCCTATAGGGCTCATGGT GTGTGCTATACTCGGGGACTTTCTGTCCGATCCATTCTCGCAGAGCTGACGGGAAGAAGA GGAGGTTGTGCTAAAGGAAAAGGAGGATCGATGCATATGTATACCAAGAACTTCTATGGG GGCAATGGCATCGTCGGTGCACAGGGCCCCCTGGGCGCTGGCATTGCTCTGGCCTGTAAA TATAAAGGAAACGATGAGATCTGTTTGACTTTATATGGGGATGGCGCTGCGAATCAGGGG CAGATAGCCGAAGCTTTCAATATGGCAGCTTTATGGAAATTACCTTGTGTTTTCATCTGT GAGAATAACCTATATGGAATGGGAACATCTACTGAGAGAGCAGCAGCCAGCCCTGATTAC TACAAGAGGGGCAATTTTATCCCTGGGCTAAAGGTCGATGGAATGGATGTTCTGTGTGTT CGTGAGGCAACAAAATTTGCAGCTAACTACTGTAGATCTGGAAAGGGGCCCATACTGATG GAGCTGCAAACCTACCGTTATCATGGACACAGTATGAGTGATCCTGGAGTCAGTTATCGT ACACGAGAAGAAATTCAGGAAGTAAGAAGTAAGAGGGATCCTATAATAATTCTCCAAGAT AGAATGGTAAACAGCAAGCTCGCCACTGTGGAAGAATTAAAGGAAATTGGGGCTGAGGTG AGGAAAGAAATTGATGATGCTGCCCAGTTTGCTACCACTGATCCTGAGCCACATTTGGAA GAATTAGGCCATCACATCTACAGCAGTGATTCATCTTTTGAAGTTCGTGGTGCAAATCCA TGGATCAAGTTTAAGTCCGTCAGTTAA |
| GenBank Gene ID | M86808 |
| GeneCard ID | None |
| GenAtlas ID | PDHA2 |
| HGNC ID | HGNC:8807 |
| Chromosome Location | 4 |
| Locus | 4q22-q23 |
| References |
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