Ceramide glucosyltransferase
Name | Ceramide glucosyltransferase |
---|---|
Synonyms | 2.4.1.80 GCS GLCT-1 Glucosylceramide synthase UDP-glucose ceramide glucosyltransferase UDP-glucose:N-acylsphingosine D-glucosyltransferase |
Gene Name | UGCG |
Organism | Human |
Amino acid sequence | >lcl|BSEQ0016105|Ceramide glucosyltransferase MALLDLALEGMAVFGFVLFLVLWLMHFMAIIYTRLHLNKKATDKQPYSKLPGVSLLKPLK GVDPNLINNLETFFELDYPKYEVLLCVQDHDDPAIDVCKKLLGKYPNVDARLFIGGKKVG INPKINNLMPGYEVAKYDLIWICDSGIRVIPDTLTDMVNQMTEKVGLVHGLPYVADRQGF AATLEQVYFGTSHPRYYISANVTGFKCVTGMSCLMRKDVLDQAGGLIAFAQYIAEDYFMA KAIADRGWRFAMSTQVAMQNSGSYSISQFQSRMIRWTKLRINMLPATIICEPISECFVAS LIIGWAAHHVFRWDIMVFFMCHCLAWFIFDYIQLRGVQGGTLCFSKLDYAVAWFIRESMT IYIFLSALWDPTISWRTGRYRLRCGGTAEEILDV |
Number of residues | 394 |
Molecular Weight | 44853.255 |
Theoretical pI | 7.86 |
GO Classification |
Functions
ceramide glucosyltransferase activity Processes
glycosphingolipid biosynthetic process glucosylceramide biosynthetic process positive regulation of protein targeting to mitochondrion small molecule metabolic process epidermis development sphingolipid metabolic process glycosphingolipid metabolic process Components
membrane integral component of membrane Golgi membrane |
General Function | Ceramide glucosyltransferase activity |
Specific Function | Catalyzes the first glycosylation step in glycosphingolipid biosynthesis, the transfer of glucose to ceramide. May also serve as a "flippase". |
Transmembrane Regions | 11-32 196-215 288-304 310-328 349-369 |
GenBank Protein ID | 1325917 |
UniProtKB ID | Q16739 |
UniProtKB Entry Name | CEGT_HUMAN |
Cellular Location | Golgi apparatus membrane |
Gene sequence | >lcl|BSEQ0016106|Ceramide glucosyltransferase (UGCG) ATGGCGCTGCTGGACCTGGCCTTGGAGGGAATGGCCGTCTTCGGGTTCGTCCTCTTCTTG GTGCTGTGGCTGATGCATTTCATGGCTATCATCTACACCCGATTACACCTCAACAAGAAG GCAACTGACAAACAGCCTTATAGCAAGCTCCCAGGTGTCTCTCTTCTGAAACCACTGAAA GGGGTAGATCCTAACTTAATCAACAACCTGGAAACATTCTTTGAATTGGATTATCCCAAA TATGAAGTGCTCCTTTGTGTACAAGATCATGATGATCCAGCCATTGATGTATGTAAGAAG CTTCTTGGAAAATATCCAAATGTTGATGCTAGATTGTTTATAGGTGGCAAAAAAGTTGGC ATTAATCCTAAAATTAATAATTTAATGCCAGGATATGAAGTTGCAAAGTATGATCTTATA TGGATTTGTGATAGTGGAATAAGAGTAATTCCAGATACGCTTACTGACATGGTGAATCAA ATGACAGAAAAAGTAGGCTTGGTTCACGGGCTGCCTTACGTAGCAGACAGACAGGGCTTT GCTGCCACCTTAGAGCAGGTATATTTTGGAACTTCACATCCAAGATACTATATCTCTGCC AATGTAACTGGTTTCAAATGTGTGACAGGAATGTCTTGTTTAATGAGAAAAGATGTGTTG GATCAAGCAGGAGGACTTATAGCTTTTGCTCAGTACATTGCCGAAGATTACTTTATGGCC AAAGCGATAGCTGACCGAGGTTGGAGGTTTGCAATGTCCACTCAAGTTGCAATGCAAAAC TCTGGCTCATATTCAATTTCTCAGTTTCAATCCAGAATGATCAGGTGGACCAAACTACGA ATTAACATGCTTCCTGCTACAATAATTTGTGAGCCAATTTCAGAATGCTTTGTTGCCAGT TTAATTATTGGATGGGCAGCCCACCATGTGTTCAGATGGGATATTATGGTATTTTTCATG TGTCATTGCCTGGCATGGTTTATATTTGACTACATTCAACTCAGGGGTGTCCAGGGTGGC ACACTGTGTTTTTCAAAACTTGATTATGCAGTCGCCTGGTTCATCCGCGAATCCATGACA ATATACATTTTTTTGTCTGCATTATGGGACCCAACTATAAGCTGGAGAACTGGTCGCTAC AGATTACGCTGTGGGGGTACAGCAGAGGAAATCCTAGATGTATAA |
GenBank Gene ID | D50840 |
GeneCard ID | None |
GenAtlas ID | UGCG |
HGNC ID | HGNC:12524 |
Chromosome Location | 9 |
Locus | 9q31 |
References |
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Related FRC
FRCD ID | Name | Exact Mass | Structure |
---|---|---|---|
Fumonisin B1 |
721.838 |